ABSTRACT

Aggressive angiomyxoma is a rare, slow-growing neoplasm of female pelvic soft tissues occurring almost exclusively in women of reproductive age. It is non-malignant but can be locally aggressive and frequently recurs. Misdiagnosis is frequent. Wide excision is the preferred method of treatment but the challenge is to perform the degree of extirpation necessary to prevent recurrence without causing unnecessary morbidity. We present a case of a 45-year-old woman who presented with a non-painful mass in the right labium majus which was causing her difficulty in walking. The resected tumour weighed 4210 g. Details of the operative procedure are given. Diagnosis was by microscopy and immunochemistry. Though rare, aggressive angiomyxoma should be considered in any young woman presenting with a well-defined mass arising from the perineum, vulva or lower pelvis.